Multiple, multifocal odontogenic keratocysts in non-syndrome patient: a case-report.

نویسندگان

  • Reshma Hammannavar
  • Kiran Holikatti
  • Sharan Bassappa
  • Nagesh Shinde
  • Manjunath Reddy
  • Y S Chidambaram
چکیده

Occurrence of multiple odontogenic keratocyst involving the jaws is rare. When multiple, it is usually associated with a syndrome. Occurrence of multiple odontogenic keratocyst without syndromic association is extremely rare. Gorlin-Goltz syndrome which is also known as Nevoid Basal Cell Carcinoma Syndrome is a rare autosomal dominant disorder. Multiple Odontogenic Keratocysts (OKCs) are principle features of nevoid basal cell carcinoma syndrome (NBCCS; Gorlin-Goltz syndrome). However, a case of multiple odontogenic keratocysts unassociated with any syndrome is reported here so as to add to the growing number of such cases in the literature. The possibility of this case being a partial expression of the Gorlin-Goltz syndrome is discussed.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

گزارش موردی ازکراتوسیست های ادنتوژنیک متعدد در سندرم گورلین

Introduction: Gorlin syndrome is a rare disorder with different diagnostic criteria such as mul-tiple odontogenic keratocysts, basal cell carcinomas, palmar &plantar pits, frontal bossing and hypertelorism and calcification of falx cerebri. Case Report: The case which is reported in the present study was a 27-years old woman re-ferred by a general dentist to oral medicine department of Hamada...

متن کامل

Bilateral Dentigerous Cysts in a Non-Syndromic Patient: Literature Review and Report of a Case

Introduction: Dentigerous cysts (DCs) are the most common developmental cysts of the jaws, mostly associated with impacted third molars and canines. Multiple or bilateral DCs are rare and typically occur in association with some syndromes including cleidocranial dysplasia and Gorlin-Goltz. The occurrence of multiple DCs is rare in the absence of these syndromes. Case Presentation: A 28-year-ol...

متن کامل

Conservative Management of Ovarian Fibroma in A Case of Gorlin-Goltz Syndrome Comorbid with Endometriosis

Ovarian fibromas are the most common benign solid ovarian tumors, which preoperative diagnosis often is difficult. Ovarian fibromas, especially in bilateral cases, may be representative of Gorlin syndrome.Gorlin syndrome (GS) is a rare autosomal dominant disorder with predisposition to basal cell carcinomas (BCCs) and other various benign and malignant tumors. To report a case of a young patien...

متن کامل

Non-Syndromic Recurrent Multiple Odontogenic Keratocysts: A Case Report

Odontogenic keratocysts (OKCs) are one of the most frequent features of nevoid basal cell carcinoma syndrome (NBS). It is linked with mutation in the PTCH gene. Partial expression of the gene may result in occurrence of only multiple recurring OKC. Our patient presented with nine cysts with multiple recurrences over a period of 11 years without any other manifestation of the syndrome.

متن کامل

Bilateral Adenomatoid Odontogenic Tumor: A rare case report

p.p1 {margin: 0.0px 0.0px 8.0px 0.0px; font: 12.0px Times} Abstract   Background and Aim:  Adenomatoid Odontogenic Tumor (AOT) accounts for less than 3% of all odontogenic tumors. It commonly occurs in anterior region of maxilla associated with an impacted tooth. Multifocal odontogenic lesions are uncommon and have only been observed in conditions associated with known genetic mutations. To...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Oral health and dental management

دوره 13 2  شماره 

صفحات  -

تاریخ انتشار 2014